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Outpatient Management Issues in Sickle Cell Disease
Reprinted by Permission of Kenneth R. Bridges, M.D. of the
Joint
Center for Sickle Cell and Thalassemic Disorders
Overview
Transition between Pediatric & Adult Care
Day Hospital
Health Maintenance
Social Services
Genetic Counseling
References
Genetic Counseling
Everyone should make informed decisions about reproduction. As with other people with genetic disorders, patients with sickle cell disease have a number of issues that are specific to their condition. People who are considering children should know about the probabilities of significant genetic disorders in those children. This information requires knowledge about the genotype of both patient and partner. Counseling should be done by trained professionals, and should be non-directive. Our job as health providers is to provide the information relevant to the decision. The patient and partner should then be free to choose the path most comfortable to them.
References
- Gaston MH, Verter JI, Woods G, et al. 1986. Prophylaxis with oral penicillin in children with sickle cell anemia. A randomized trial. N Engl J Med 314: 1593-1599.
- Falletta JM, Woods GM, Verter JI, et al. 1995. Discontinuing penicillin prophylaxis in children with sickle cell anemia. Prophylactic Penicillin Study II. J Pediatr 127:685-690.
- Wong WY, Powars DR, Chan L, et al. 1992. Am J Hematol 39:176-82.
- Ambrosino DM, Landesman SH, Gorham, CC, Siber GR. 1986. Passive immunization against disease due to Haemophilus influenzae type b: concentrations of antibody to capsular polysaccharide in high-risk children. J Infect Dis 153: 1-7.
- Raichand M, Goldberg MF, Nagpal KC, Goldbaum, MH, Asdourian GK. 1977. Evolution of neovascularization in sickle cell retinopathy. A prospective fluorescein angiographic study. Arch Opthalmol 95:1543-1552.
- Rosse WF, Gallagher D, Kinney TR, et al. 1990. Transfusion and alloimmunization in sickle cell disease. The Cooperative Study of Sickle Cell Disease. Blood 76:1431-1437.
- Ohaeri JU, Shokunbi WA, Akinlade KS, Dare, LO. 1995. The psychosocial problems of sickle cell disease sufferers and their methods of coping. Soc Sci Med 40: 955-960.
- Barbarin OA, Whitten CF, Bonds SM. 1994. Estimating rates of psychosocial problems in urban and poor children with sickle cell anemia. Health Soc Work 19:112-119.
- McCrae JD, Lumley MA. 1998. Health status in sickle cell disease: examining the roles of pain coping strategies, somatic awareness, and negative affectivity. J Behav Med 21:35-55
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